When AIED is limited to the ear, it is called “primary AIED.” In approximately 15-30% of cases, AIED occurs within the context of systemic autoimmune disease, it is called “secondary AIED.” 1 Examples of autoimmune disorders that can cause secondary AIED include Cogan's syndrome, granulomatosis with polyangiitis (GPA), ...
Autoimmune inner ear disease (AIED), is a rare disease that happens when your body's immune system mistakenly attacks your inner ear. It can cause dizziness, ringing in your ears, and hearing loss. Less than 1% of the 28 million Americans who have hearing loss have it because of AIED.
Autoimmune inner ear disease (AIED) is a reversible form of sensorineural hearing loss when immunosuppressive treatment is given.
Possible Meniere's disease causes: Genetics — People with a family history of the condition are more likely to develop Meniere's disease. Irregular immune response — A weakened immune system can result in an abnormal response to infections. Some researchers believe that Meniere's disease is an autoimmune disorder.
Vertigo and other audiovestibular symptoms may be the first manifestation of an autoimmune disease and if correctly addressed could significantly contribute to early diagnosis of the underlying autoimmune disease.
Autoimmune diseases can affect many types of tissues and nearly any organ in your body. They may cause a variety of symptoms including pain, tiredness (fatigue), rashes, nausea, headaches, dizziness and more.
Ultimately, many diagnose AIED by the positive response to steroid treatment. Steroids (dexamethasone, prednisone, prednisolone) are often used for the treatment of AIED. High doses, often in doses of 40-80 gm/day, may be useful in the initial management of AIED.
AIED is rare and diagnosed only when all other causes have been ruled out. The estimated prevalence of AIED is about 15 out of 100,000 people. AIED is felt to be responsible for less than one percent of all SNHL cases, realizing many AIED cases might not be diagnosed due to lack of specific tests.
Tinnitus causes
In AIED, the body's immune system attacks the inner ear. This results in damage that can cause tinnitus. While it is possible to have AIED on its own, 15 to 30 percent of those with AIED have other autoimmune disorders.
Autoimmune inner ear disease (AIED)
Similar to Meniere's disease, there are many aspects of AIED diagnosis and management that remain unclear, though research is ongoing.
Cogan's syndrome is a rare autoimmune disease that primarily affects the eyes and inner ears, but can also cause inflammation of the blood vessels—a condition known as vasculitis.
The main two types of inner ear infections are labyrinthitis and vestibular neuritis. Both of these inner ear infections can cause a number of symptoms, including vertigo, dizziness, and nausea. A person with labyrinthitis may also experience hearing issues.
Common inner ear balance disorders include: Benign paroxysmal positional vertigo (BPPV), also known as positional vertigo, is a dizzy or spinning sensation in your head, and is the most common type of vertigo.
Autoimmune sensorineural hearing loss (SNHL) is a rare clinical entity characterized by a progressive fluctuating bilateral asymmetric SNHL that develops over several weeks to months. Vestibular symptoms, tinnitus and aural fullness are present in up to 50% of patients.
How do you fix an inner ear infection? Sometimes, your healthcare provider may prescribe antivirals or antibiotics to treat your inner ear infection. More often, however, they'll focus on treating your symptoms rather than the infection itself. For example, steroids are often prescribed to ease inflammation.
Vitamin A, C, and E
The antioxidants in these vitamins prevent damage to health cells, making all three of these essential vitamins for ear health. Vitamin C also bolsters the immune system, which can reduce the risk of pesky ear infections.
The symptoms of AIED are sudden hearing loss in one ear progressing rapidly to the second ear. The hearing loss can progress over weeks or months. Patients may feel fullness in the ear and experience vertigo. In addition, a ringing, hissing, or roaring sound in the ear may be experienced.
Antinuclear antibodies are markers for a number of autoimmune diseases, the most notable of which is systemic lupus erythematosus (Ferrell and Tan, 1985). Antibodies to specific nuclear constituents are high specific for certain collagen vascular diseases.