Kluver-Bucy syndromeKlüver-Bucy syndrome is a rare behavioral impairment that is associated with damage to both of the anterior temporal lobes of the brain. It causes individuals to put objects in their mouths and engage in inappropriate sexual behavior.https://www.ninds.nih.gov › disorders › kluver-bucy-syndrome
What causes Klüver-Bucy syndrome? Klüver-Bucy syndrome happens when your brain's temporal lobes, especially your hippocampus and amygdala, are injured. Brain damage may be due to traumatic head injury, infection or disease. Adults are most likely to develop KBS due to stroke or head injury.
Klüver-Bucy syndrome is a rare behavioral impairment that is associated with damage to both of the anterior temporal lobes of the brain. It causes individuals to put objects in their mouths and engage in inappropriate sexual behavior.
Title: Hyperorality Definition: A tendency or compulsion to examine objects by mouth.
In a series of different procedures and tests on 16 monkeys, Klüver and Bucy found that monkeys with bilateral temporal lobe surgery often had the following symptoms: Psychic Blindness - This is a term that signifies a lack of meaning in what was being viewed, and the monkey would view the same object over and over.
Urbach-Wiethe syndrome is a rare autosomal recessive disorder predisposing to increased collagen deposition in the skin and soft tissues. Characteristic features include monoliform blepharosis, ankyloglossia and bilateral symmetric basal ganglia calcification.
In Alzheimer's disease, the amygdala is generally affected later than the hippocampus. So a person with Alzheimer's will often recall emotional aspects of something even if they don't recall the factual content.
Pick's disease is a type of frontotemporal dementia, a neurodegenerative disease. That means the affected neurons (brain or nerve cells) gradually stop working. As brain cells in the affected areas fail, those areas atrophy (shrink or wither), and you lose the abilities those areas once controlled.
Pick's disease is caused by a buildup of tau proteins, called “Pick bodies,” in the brain. Pick bodies cause neurological damage in areas where they are present, which includes (but is not limited to) the frontal lobes.
People with FTD have abnormal substances (called tangles, Pick bodies, Pick cells, and tau proteins) inside nerve cells in the damaged areas of the brain. The exact cause of the abnormal substances is unknown. Many different abnormal genes have been found that can cause FTD.
Understanding Damage to the Amygdala
The amygdala in particular controls the body's response to fear and emotional and behavioral regulation. When the amygdala sustains damage, it can cause difficulty with memory processing, emotional reactions, and decision-making.
S.M., also sometimes referred to as SM-046, is an American woman with a peculiar type of brain damage that prevents her from experiencing fear. First described by scientists in 1994, she has had exclusive and complete bilateral amygdala destruction since late childhood as a consequence of Urbach–Wiethe disease.
The patient, a woman in her 40s known as SM, has an extremely rare condition called Urbach-Wiethe disease that has caused extensive damage to the amygdala, an almond-shaped area in the brain long known for its role in fear.
Gerstmann's syndrome is a cognitive impairment that results from damage to a specific area of the brain -- the left parietal lobe in the region of the angular gyrus. It may occur after a stroke or in association with damage to the parietal lobe.
Causes of frontotemporal dementia
Frontotemporal dementia is caused by clumps of abnormal protein forming inside brain cells. These are thought to damage the cells and stop them working properly. The proteins mainly build up in the frontal and temporal lobes of the brain at the front and sides.
The amygdalae. Findings from animal studies have clearly demonstrated that within the temporal lobe it is the amygdala that is the pivotal structure in mediating sexual behaviour. A recent study has directly examined the role of the amygdala in human sexual functioning.
Definition. Binswanger's disease (BD), also called subcortical vascular dementia, is a type of dementia caused by widespread, microscopic areas of damage to the deep layers of white matter in the brain.
Lewy body dementia causes a progressive decline in mental abilities. People with Lewy body dementia might have visual hallucinations and changes in alertness and attention. Other effects include Parkinson's disease signs and symptoms such as rigid muscles, slow movement, walking difficulty and tremors.
The most common signs of frontotemporal dementia involve extreme changes in behavior and personality. These include: Increasingly inappropriate social behavior. Loss of empathy and other interpersonal skills, such as having sensitivity to another's feelings.
Pseudodementia (fake dementia or fake cognitive decline) occurs when a person is so slowed down from depression or another psychiatric illness that they present as intellectually or cognitively impaired.
Other conditions which may cause or mimic dementia include depression, brain tumors, nutritional deficiencies, head injuries, hydrocephalus, infections (AIDS, meningitis, syphilis), drug reactions and thyroid problems.
Lewy bodies were rare in neurodegenerative diseases where the amygdala is not heavily involved by the disease process (ALS and PSP).
Amygdala atrophy is prominent in early Alzheimer's disease and relates to symptom severity.
Schizophrenia patients demonstrated a deficit in amygdala reactivity to negative face stimuli and an alteration, correlated with neuroleptic drug dosage, in the functional coupling between the amygdala and subgenual cingulate.